CLINICAL, X-RAY AND COMPUTER-TOMOGRAPHIC PICTURE OF DESMOPLASTIC FIBROMA OF THE LOWER JAW IN CHILDREN

Sergey Chuykin; Nail' Davletshin; Oleg Chuykin; Khadyatullo Ayubov; Akbar Shodiev; Kristina Kuchuk

doi:10.18481/2077-7566-21-17-3-101-107

UDC 61

CLINICAL, X-RAY AND COMPUTER-TOMOGRAPHIC PICTURE OF DESMOPLASTIC FIBROMA OF THE LOWER JAW IN CHILDREN

Published in Actual problems in dentistry · Volume 17, Issue 3 · Pages 101–107 · Rubric: PEDIATRIC DENTISTRY, PROPHILAXIS AND ORTODONTICS

DOI: https://doi.org/10.18481/2077-7566-21-17-3-101-107

Received: 04.11.2021 Accepted: 27.11.2025 Language of publication: RUS

Authors

Sergey Chuykin

ORCID

Nail' Davletshin

Oleg Chuykin

Khadyatullo Ayubov

et al.

Akbar Shodiev

Kristina Kuchuk

ORCID

Sergey Chuykin

Academic degree: doctor of medical sciences

Science rang: professor

Bashkir State Medical Universitey Head of the Department · Department of Pediatric Dentistry and Orthodontics · Russian Federation · Ufa

ORCID

Nail' Davletshin

Academic degree: doctor of medical sciences

Science rang: docent

Bashkir State Medical University Professor of Department · Department of Pediatric Dentistry and Orthodontics with a course of IAPE · Russian Federation · Ufa

Oleg Chuykin

Bashkir State Medical University, Ufa, Russia assistant of the professor · Department of Children's Dentistry and Orthodontics · Russian Federation · Ufa

Khadyatullo Ayubov

Bashkir State Medical University Assistant of the department · Department of Pediatric Dentistry and Orthodontics with IAPE course · Russian Federation · Ufa

Republican Children's Clinical Hospital Head of the Department · Pediatric Maxillofacial Surgery · Russian Federation · Ufa

Akbar Shodiev

Republican Children's Clinical Hospital Clinical Resident · Department of Oral and Maxillofacial Surgery · Russian Federation · Ufa

Kristina Kuchuk

Bashkir State Medical University assistant · Head of the Department of Pediatric Dentistry and Orthodontics · Russian Federation · Ufa

ORCID

ABSTRACT

The paper presents the results of a clinical observation of a 6-year-old female patient, who was admitted to the department of maxillofacial surgery of a multidisciplinary hospital under the compulsory health insurance system with a rare disease of the bone tissue of the lower jaw – desmoplastic fibroma. Desmoplastic fibroma of bone tissue (aggressive fibromatosis, desmoid fibroma) is a rare, locally aggressive, benign tumor localized in bone tissue, it is a mesenchymal fibroproliferative tumor with locally destructive growth, accounting for less than 0.03% of all human tumors. According to the literature, desmoplastic fibroma has a recurrence rate of 37% to 72%, resection of the affected bone is the preferred therapy, and, ideally, resection should be a single resection block. Wide excision is the method of choice for treating operable desmoid tumors in children. The article presents a dynamic observation within 1 year after surgical treatment. The article presents the clinical, radiological and computed tomographic picture of the disease and the results of instrumental and histological examination of a rare oncostomatological pathology. Purpose: clinical, radiological, 3D computed tomography observation of a child with desmoplastic fibroma of the lower jaw. Materials and methods: the results of a clinical examination, instrumental methods of X-ray diagnostics, stages of surgical treatment, a histological report and photographs of the patient's appearance are presented. Conclusion: Given the high regenerative capacity of bone tissue in children, it is necessary to perform surgical treatment of benign neoplasms by the type of marginal resection, that is, by the organ-preserving type, and to conduct dispensary observation of the patient during the first year.

KEYWORDS

maxillofacial surgery, desmoid fibromatosis, desmoid, neoplasm of the maxillofacial region, X-ray diagnostics

Funding

No financial support has been provided for this work

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GOST

Chuykin S. V., Davletshin N. A., Chuykin O. S., Ayubov K. H., Shodiev A. A., Kuchuk K. N. CLINICAL, X-RAY AND COMPUTER-TOMOGRAPHIC PICTURE OF DESMOPLASTIC FIBROMA OF THE LOWER JAW IN CHILDREN // Actual problems in dentistry. 2021. no. 3. pp. 101-107. DOI: https://doi.org/10.18481/2077-7566-21-17-3-101-107. (Date of access 08.10.2026).

MLA

Sergey Chuykin, Davletshin N. A., Chuykin O. S., Ayubov K. H., Shodiev A. A., Kuchuk K. N.. "CLINICAL, X-RAY AND COMPUTER-TOMOGRAPHIC PICTURE OF DESMOPLASTIC FIBROMA OF THE LOWER JAW IN CHILDREN." Actual problems in dentistry 17.3 (2021): 101-107. DOI: https://doi.org/10.18481/2077-7566-21-17-3-101-107.

APA

Chuykin S. V., Davletshin N. A., Chuykin O. S., Ayubov K. H., Shodiev A. A., Kuchuk K. N. (2021). CLINICAL, X-RAY AND COMPUTER-TOMOGRAPHIC PICTURE OF DESMOPLASTIC FIBROMA OF THE LOWER JAW IN CHILDREN. Actual problems in dentistry, 17(3), 101-107. https://doi.org/10.18481/2077-7566-21-17-3-101-107

Chicago

Sergey Chuykin, Davletshin N. A., Chuykin O. S., Ayubov K. H., Shodiev A. A., Kuchuk K. N.. "CLINICAL, X-RAY AND COMPUTER-TOMOGRAPHIC PICTURE OF DESMOPLASTIC FIBROMA OF THE LOWER JAW IN CHILDREN." Actual problems in dentistry 17, no. 3 (2021): 101-107. https://doi.org/10.18481/2077-7566-21-17-3-101-107.

WIKI

{{cite journal | author = Chuykin S. V., Davletshin N. A., Chuykin O. S., Ayubov K. H., Shodiev A. A., Kuchuk K. N. | title = CLINICAL, X-RAY AND COMPUTER-TOMOGRAPHIC PICTURE OF DESMOPLASTIC FIBROMA OF THE LOWER JAW IN CHILDREN | journal = Actual problems in dentistry | year = 2021 | volume = 17 | issue = 3 | pages = 101-107 | doi = 10.18481/2077-7566-21-17-3-101-107 }}

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