Krasnoyarsk Scientific Center of the Siberian Branch of the Russian Academy of Sciences
Krasnoyarsk, Krasnoyarsk, Russian Federation
Krasnoyarsk, Krasnoyarsk, Russian Federation
Krasnoyarsk, Krasnoyarsk, Russian Federation
Sharypovo, Krasnoyarsk, Russian Federation
Krasnoyarsk, Krasnoyarsk, Russian Federation
Krasnoyarsk, Krasnoyarsk, Russian Federation
Subject. Cleidocranial dysplasia is a rare hereditary pathology found in general and dental clinical practice. According to current data in the world literature, to date about 500 cases of this disease have been described. Purpose — increased effectiveness of diagnostic maneuverin patients with cleidocranialdysplasia in clinical dental practice. Methodology. In order to ensure the regularization and systematization of scattered clinical and diagnostic information on the pathology studied, a meta-analysis of native and foreign reference, scientific and educational and methodological literary sources related to this problem has been carried out. Patients with cleidocranial dysplasia were examined, the formed diagnostic algorithm was tested, clinical manifestation of pathology was evaluated. Results. As a result of the analysis, a convenient and practically acceptable model of the main clinical signs of cleidocranialdysplasia has been developed for the formation of a diagnostic algorithm for dental practitioners. Two clinical cases are presented showing the results of the diagnostic process in patients with cleidocranialdysplasia, complex and questionableclinical situations in the oral cavity. Conclusion. The model of the main clinical signs of cleidocranial dysplasia is an effective diagnostic algorithm in dental practice, which forms in practical dentists professional skills and competence in routing and attracting to advise specialists of related specialties of dental and general medical profiles, in cases of detection of patients with this rarely occurring pathology on clinical reception. The presented clinical cases demonstrate the effectiveness of its application in the practice of the dentist, illustrating a detailed, competent and acceptable scheme of writing the history of the disease of patients with this pathology, complex and questionable clinical situations of a universal nature and in the oral cavity in the outpatient dentalappointment.
cleidocranial dysplasia, cleidocranialdysostosis, Scheuthauer — Marie —Sainton syndrome, congenital pathology of maxillofacial area, dental impaction, supplementary tooth, delay of change of temporary teeth
Статья ретрагирована.
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